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TL;DR
This case report describes a pediatric patient with cavernous transformation of the portal vein who underwent TIPS creation for variceal hemorrhage at age 8 and returned at age 16 with incidental TIPS occlusion.
JPGN reports · 4 authors, 3 centres
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This case report describes a pediatric patient with cavernous transformation of the portal vein who underwent TIPS creation for variceal hemorrhage at age 8 and returned at age 16 with incidental TIPS occlusion.
This case report describes a pediatric patient with cavernous transformation of the portal vein who underwent TIPS creation for variceal hemorrhage at age 8 and returned at age 16 with incidental TIPS occlusion. Pre-anesthetic evaluation revealed hypoxemia to 85% and digital clubbing. At 1-year follow-up, the TIPS remained patent, and the patient was asymptomatically hypoxemic in the low 90s at rest with desaturations to the mid 80s with activity. The authors discuss potential mechanisms including increased vasoactive metabolite production from portal hypertension or decreased hepatic clearance due to liver disease or portal bypass. Liver transplantation is noted as the curative treatment for HPS.